R2. Forme particulare de angisarcomatoza Kaposi: forma buloasa (Kaposi limfangioma-like) si forma cu tumori subcutanate (kaposipseudoadenopatic)
In cadrul formelor clinice particulare ale bolii Kaposi europene sunt prezentate cazuri personale de forme buloase si forma cu tumori subcutanate.
Forma buloasa (Kaposi limfangioma-like sau cu limfangiectazii) are doua forme clinice: secundara (ce debuteaza cu leziuni tipice dupa care apar leziuni buloase) si forma primitiva (cu primele leziuni sub forma de bule). Autorii prezinta doua cazuri de forme secundare ce au debutat cu leziuni tipice si unde, dupa cativa ani de evolutie, au aparut leziuni buloase, bolnavi prezentand concomitent ambele tipuri de leziuni. Bulele erau localizate numai pe membrele inferioare, nu se insoteau de limfedem kaposian, apareau in pielea sanatoasa, unde erau sub tensiune, iar alte flasce. Histologic bula avea localizare dermo-hipodermica sub forma de ectazii limfatice (aspect limfangioma-like) cu cavitati multiple si aspect buretos. Raspuns favorabil la roentgen terapie.
Forma cu tumori subcutanate (Kaposi pseudoadenopatic), intalnita la un caz, a debutat cu leziuni tipice dupa 7 ani au aparut multiple tumorete subcutanate situate in zona poplitee si zona inghinala, cu aspect clinic de ganglioni hipertrofiati. Examenul histologic nu a aratat o structura ganglionara ci aspect de tumori subcutanate de tip Kaposian, cu o bogata componenta vasculara. Raspuns favorabil la roentgen terapie.
R2. Peculiar Types of Kaposi's Sarcoma: Bullous Type (Kaposi pseudoadenopatic)
We presented two cases of bullous types and one case with subcutaneous tumors which are peculiar types of classical Kaposi's sarcoma.
Bullous type (Kaposi lymphangioma-like or with lymphangiectasis) has two different forms: secondary (what begin with typical lesions, after which appear bullae( and primitive (which begin with bullae). The authors presents two cases of secondary forms, which begined with typical lesions and in a few years developed bullous lesions, the patients presented simultaneously both types of lesions. The bullous lesions were located only on legs, lymphedeom was not found, the blisters arise from normal skin, in tense or flaccid. Histologyc, the blister was dermo-hipodermic (lymphangioma-like) with many cavities and subcutaneous tumors (Kaposi pseudoadenopatic), one case, begin with typical lesions and after seven years developed many subcutaneous tumors in popliteal and inghinal zones, with clinical aspects of adenopathy. Histology shows tumoral aspect of Kaposi's sarcoma with important vascular component. treated with roentghetheraphy with succes.