PF9. Pustuloza subcornoasa Sneddon-Wilkinson - caz clinic
Corina Bud, F. Benedek. Florica Sarac, Constanta Turda, Simona Fratila
Clinica Dermatologie Oradea

Prezentam cazul unei paciente de 17 ani cu o eruptie pustuloasa dispusa in plaarde cu margini circinate localizate pe membre, fata posterioara a trunchiului si fese, aparuta in urma cu 14 zile de la consultul dermatologic.

Boala a debutat de la varsta de trei saptamani cu eruptii eritemato-veziculoase, in pusee recidivante, mai ales primavara si cu accentuari la soare. Dupa o cura heliomarina se instaleaza o remisiune de doisprezece ani.

Examenul histopatologic pune in evidenta o pustula subcornoasa ce contine polinucleare neutrofile si rare eozinofile. Se instituie tratament cu Dapsona 100 mg/zi urmat de disparitia leziunilor si intrarea in remisiune a bolii dupa o luna de tratament. Pustuloza subcornoasa este o afectiune rara, cronica, benigna si recidivanta ce atinge de obicei femeile de varsta medie; ocazional intalnita la copii, se dovedeste a fi o entitate clinica si histologica unica.

PF9. Subcorneal pustular dermatosis Sneddon-Wilkinson - a clinical case
Corina Bud, F. Benedek. Florica Sarac, Constanta Turda, Simona Fratila
Dermatology Clinic Oradea

We present the case of one feminine pacient about 17 years old, with a pustular eruption in circinate patterns, localized on limbs, postrior aspects of the trunk and buttocks, which appeared 14 days before the dermatological examination.

The disease started at the age of three weeks with erythematous-vesicular eruptions, which relapsed especially in spring and at sun exposures. After a climatotherapy cure with salt-water bathing, a 12 years remission occurred. At the histopathological examination, we observed subcorneal pustules filled with polymorphonuclear leukocytes and occasional eosinophiles. After one month therapy with Dapsone, 100 mg/day, the lesions disappeared and we obtained the clinical remission. Subcorneal pustular dermatosis is a rare, chronic, benign and recurrent disease, more common in women in mild ages. Just occasionaly observed in children, it is an unique clinical and histological entity.